ICD-10-CM Code E76: Disorders of glycosaminoglycan metabolism and Related Diagnosis Codes.


The ICD-10-CM (the International Classification of Diseases, Tenth Revision, Clinical Modification) is a standardized coding system used when classifying diseases and medical conditions. Healthcare providers report these codes on Medical claims when diagnosing patient care.

Explore ICD-10-CM codes, organized by chapters based on body systems and medical conditions, as outlined in the International Classification of Diseases, Tenth Revision, Clinical Modification.

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Eclaims - ICD-10-CM Tabular Code List v1.0.0

A categorized list of ICD-10-CM codes organized by chapters based on body systems or medical conditions, according to the International Classification of Diseases, Tenth Revision, Clinical Modification.

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  • E76 - Disorders of glycosaminoglycan metabolism
    • E76.0 - Mucopolysaccharidosis, type I
      • E76.01 - Hurler's syndrome
      • E76.02 - Hurler-Scheie syndrome
      • E76.03 - Scheie's syndrome
    • E76.1 - Mucopolysaccharidosis, type II
    • E76.2 - Other mucopolysaccharidoses
      • E76.21 - Morquio mucopolysaccharidoses
        • E76.210 - Morquio A mucopolysaccharidoses
        • E76.211 - Morquio B mucopolysaccharidoses
        • E76.219 - Morquio mucopolysaccharidoses, unspecified
      • E76.22 - Sanfilippo mucopolysaccharidoses
      • E76.29 - Other mucopolysaccharidoses
    • E76.3 - Mucopolysaccharidosis, unspecified
    • E76.8 - Other disorders of glucosaminoglycan metabolism
    • E76.9 - Glucosaminoglycan metabolism disorder, unspecified

Note: The International Classification of Diseases, Tenth Revision, Clinical Modification (ICD-10-CM) codes are developed and maintained by the Centers for Disease Control and Prevention (CDC). CDC's National Center for Health Statistics (NCHS) is responsible for the clinical modification of ICD-10 for use in the United States. The World Health Organization (WHO), which owns and publishes ICD-10, authorized NCHS to develop ICD-10-CM. All modifications to ICD-10 must conform to WHO's established ICD structure and conventions. All rights are reserved by the respective entities.