ICD-10-CM Code E70: Disorders of aromatic amino-acid metabolism and Related Diagnosis Codes.


The ICD-10-CM (the International Classification of Diseases, Tenth Revision, Clinical Modification) is a standardized coding system used when classifying diseases and medical conditions. Healthcare providers report these codes on Medical claims when diagnosing patient care.

Explore ICD-10-CM codes, organized by chapters based on body systems and medical conditions, as outlined in the International Classification of Diseases, Tenth Revision, Clinical Modification.

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Eclaims - ICD-10-CM Tabular Code List v1.0.0

A categorized list of ICD-10-CM codes organized by chapters based on body systems or medical conditions, according to the International Classification of Diseases, Tenth Revision, Clinical Modification.

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  • E70 - Disorders of aromatic amino-acid metabolism
    • E70.0 - Classical phenylketonuria
    • E70.1 - Other hyperphenylalaninemias
    • E70.2 - Disorders of tyrosine metabolism
      • E70.20 - Disorder of tyrosine metabolism, unspecified
      • E70.21 - Tyrosinemia
      • E70.29 - Other disorders of tyrosine metabolism
    • E70.3 - Albinism
      • E70.30 - Albinism, unspecified
      • E70.31 - Ocular albinism
        • E70.310 - X-linked ocular albinism
        • E70.311 - Autosomal recessive ocular albinism
        • E70.318 - Other ocular albinism
        • E70.319 - Ocular albinism, unspecified
      • E70.32 - Oculocutaneous albinism
        • E70.320 - Tyrosinase negative oculocutaneous albinism
        • E70.321 - Tyrosinase positive oculocutaneous albinism
        • E70.328 - Other oculocutaneous albinism
        • E70.329 - Oculocutaneous albinism, unspecified
      • E70.33 - Albinism with hematologic abnormality
        • E70.330 - Chediak-Higashi syndrome
        • E70.331 - Hermansky-Pudlak syndrome
        • E70.338 - Other albinism with hematologic abnormality
        • E70.339 - Albinism with hematologic abnormality, unspecified
      • E70.39 - Other specified albinism
    • E70.4 - Disorders of histidine metabolism
      • E70.40 - Disorders of histidine metabolism, unspecified
      • E70.41 - Histidinemia
      • E70.49 - Other disorders of histidine metabolism
    • E70.5 - Disorders of tryptophan metabolism
    • E70.8 - Other disorders of aromatic amino-acid metabolism
      • E70.81 - Aromatic L-amino acid decarboxylase deficiency
      • E70.89 - Other disorders of aromatic amino-acid metabolism
    • E70.9 - Disorder of aromatic amino-acid metabolism, unspecified

Note: The International Classification of Diseases, Tenth Revision, Clinical Modification (ICD-10-CM) codes are developed and maintained by the Centers for Disease Control and Prevention (CDC). CDC's National Center for Health Statistics (NCHS) is responsible for the clinical modification of ICD-10 for use in the United States. The World Health Organization (WHO), which owns and publishes ICD-10, authorized NCHS to develop ICD-10-CM. All modifications to ICD-10 must conform to WHO's established ICD structure and conventions. All rights are reserved by the respective entities.